3-Hydroxy-2-methylbutanoic acid, urinary metabolite (ab146014)
Key features and details
- Urinary metabolite excreted in abnormally high amounts in beta-ketothiolase deficiency
- CAS Number: 473-86-9
- Purity: > 98%
- Form / State: Solid
- Source: Synthetic
Overview
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Product name
3-Hydroxy-2-methylbutanoic acid, urinary metabolite -
Description
Urinary metabolite excreted in abnormally high amounts in beta-ketothiolase deficiency -
Alternative names
- 2-Methyl-3-hydroxybutanoate
- 2-Methyl-3-hydroxybutyric Acid
- 3-Hydroxy-2-methylbutyric Acid
see all -
Biological description
β-hydroxy carboxylic acid involved in isoleucine catabolism, as well as beta-oxidation of fatty acids and ketogenesis. Urinary metabolite excreted in abnormally high amounts in beta-ketothiolase deficiency.
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Purity
> 98% -
CAS Number
473-86-9 -
Chemical structure
Properties
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Molecular weight
118.13 -
Molecular formula
C5H10O3 -
Storage instructions
Store at -20°C. Store under desiccating conditions. The product can be stored for up to 12 months. -
Handling
Wherever possible, you should prepare and use solutions on the same day. However, if you need to make up stock solutions in advance, we recommend that you store the solution as aliquots in tightly sealed vials at -20°C. Generally, these will be useable for up to one month. Before use, and prior to opening the vial we recommend that you allow your product to equilibrate to room temperature for at least 1 hour.
Need more advice on solubility, usage and handling? Please visit our frequently asked questions (FAQ) page for more details.
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Source
Synthetic